Inguinal mass is a common clinical finding or even symptom in childhood while the most common diagnosis is inguinal hernia that may proceed with prompt surgical but there are a vast variety of different entities that may manifest as an inguinal mass and in some instances, surgical approach is not indicated or may need further preoperative assessments to determine a correct therapeutic plan. In this article, we discuss about an example of unusual case of extrarenal Wilms tumor in inguinal region which was presented as an inguinal mass and also review differential diagnosis for childhood inguinal mass.